Multiple muscle hypoplasia in Poland's syndrome [Multipl kas hipoplazili Poland sendromu]

Abstract

Poland's syndrome is a nonhereditary congenital disorder with unknown etiology, characterized by unilateral absence of pectoralis major muscle and various deformities of the ipsilateral upper extremity. The most common muscle abnormalities accompanying pectoralis major muscle deficiency are the hypoplasia of the pectoralis minor, latissimus dorsi, serratus anterior, teres major and other thoracic muscles.(1,2,3). When muscles of the back are also hypoplastic, scapulathoracic joint dysfunction occurs, resulting in a decrease in the power of the shoulder muscles. In our case, the pectoralis major and minor, and serratus anterior muscles were severely hypoplastic. The proximal aspect of the trapezius, rhomboids and shoulder rotators were atrophic. In addition to decreased muscle power in the shoulder, the patient had winged scapula deformity.